Canavan Disease:From Spongy Degeneration to Molecular Analysis
J Pediatr 127:511-517, Matalon,R.,et al, 1995
Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Creutzfeldt-Jakob Disease (Subacute Spongiform Encephalopathy)
Adams & Victors Principles of Neurology, Chp 33, pg 769, Ropper, A.H.,et al, 2014
Inherited Metabolic Diseases of the Nervous System, Subacute Necrotizing Encephalopathy (Leigh Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 996, Ropper, A.H.,et al, 2014
Cortical Restricted Diffusion as the Predominant MRI Finding in Sporadic Creutzfeldt-Jakob Disease
Acta Radiologica 52:336-339, Talbott,S.D.,et al, 2011
Clinicopath conf., Human Prion Disease, Sporadic CJD
Neurol 69:1881-1887, Geschwind,M.D., et al, 2007
Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
NEJM 339:1994-2004, Johnson,R.T. & Gibbs,Jr.,C.J., 1998
A New Variant of Creutzfeldt-Jakob Disease in the UK
Lancet 347:921-925, 915, 916, 91796., Will,R.G.,et al, 1996
Leigh Syndrome:Clinical Features and Biochemical DNA Abnormalities
Ann Neurol 39:343-351, Rahman,S.,et al, 1996
Infantile CNS Spongy Degeneration-14 Cases:Clinical Update
Neurol 40:1876-1882, Gascon,G.G.,et al, 1990
Familial Alzheimer's Disease with Myoclonus and'Spongy Change'
Arch Neurol 45:1097-1100, Duffy,P.,et al, 1988
Diffuse Lewy Body Disease and Progressive Dementia
Neurol 38:1520-1528, Burkhardt,C.R.,et al, 1988
Leukoencephalopathy After Inhaling"Heroin"Pyrolysate
Lancet 2:1233-1237, Wolters,E.C.,et al, 1982
Leukoencephalopathy in Childhood Leukemia
et al. , Neurol 27:609977., Devivo,D.C., 1977
Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Gertsmann-Straussler Schneinker Syndrome
Adams & Victors Principles of Neurology, Chp 33, pg 773, Ropper, A.H.,et al, 2014
Transmissible Spongiform Encephalopathy in the 21st Century: Neuroscience for the Clinical Neurologist
Neurol 70:713-722, Brown,P., 2008
Heroin-Induced Spongiform Leukoencephalopathy: Value of Diffusion MF Imaging
J Comput Assist Tomog 24:735-737, Chen,C.,et al, 2000
Progressive Aphasia with Rapidly Progressive Dementia in a 49 Year Old Woman
JNNP 66:238-243, Greene,J.D.W.,et al,, 1999
Surgical Treatment and Risk of Sporadic Creutzfeldt-Jakob Disease:A Case-Control Study
Lancet 353:693-697, Collins,S.,et al, 1999
Risk of Transmission of Bovine Spongiform Encephalopathy to Humans in the United States, Report of the Council on Scientific Affairs
JAMA 281:2330-2339, Tan,L.,et al, 1999
Heroin Inhalation and Progressive Spongiform Leukoencephalopathy
Neurol 48:589-590, Kriegstein,A.R.,et al, 1997
New Variant Creutzfeldt-Jakob Disease:Neurological Features and Diagnostic Tests
Lancet 350:903-907, Zeidler,M.,et al, 1997
Transmissible Spongiform Encephalopathies
NEJM 337:1821-1828, Haywood,A.M., 1997
Clinical, Neuroimaging, and Pathologic Features of Progressive Nonfluent Aphasia
Ann Neurol 39:166-173, Turner,R.S.,et al, 1996
Creutzfeldt-Jakob Disease and Bovine Spongiform Encephalopathy:Any Connection?
BMJ 311:1415-1421, Almond,J.W., 1995
Real and Imagined Clinicopathological Limits of"Prior Dementia"
Lancet 341:127-129, Brown,P.,et al, 1993
Infectious Prions or Cytotoxic Metabolites?
Lancet 341:159-161, Pablos-Mendez,A.,et al, 1993
Progressive Language Disorder Due to Lobar Atrophy
Ann Neurol 31:174-183, Snowden,J.S.,et al, 1992
The Spongiform Encephalopathies, Editorial
JNNP 54:761-763, Will,R.G., 1991
Creutzfeldt-Jakob Disease and Other Transmissible Spongiform Encephalopathies
Ed, F. O. Bastian, Mosby Year Book, St. Louis 9:153, Maertens,P.&Quindlen,E.A., 1991
Diagnosis of Gerstmann-Straussler Syndrome in Familial Dementia with Prion Protein Gene Analysis
Lancet 2:15-17, Collinge,J.,et al, 1989
Leigh Disease (Subacute Necrotizing Encephalomyelopathy) :CT & MR in Five Cases
J Comput Assist Tomogr 12:40-44, Geyer,C.A.,et al, 1988
Gerstmann-Straussler-Scheinker Disease:Autopsy Study of a Familial Case
Ann Neurol 20:540-543, Vinters,H.V.,et al, 1986
Creutzfeldt-Jakob Disease after Administration of Human Growth Hormone
Lancet 2:244-246, Powell-Jackson,J.,et al, 1985
Gerstmann-Straussler-Scheinker Disease with Coincidental Familial Onset
Ann Neurol 14:670-678, Hudson,A.J.,et al, 1983
Computerized Cranial Tomography in Cerebral Diseases of White Matter
Neurol 28:534, Lane,B.,et al, 1978
Clinical Pathologic Conference, Creutzfeldt-Jakob Disease, (Case record 43-1977)
NEJM 297:930, Scully,R.E.,et al, 1977